A fatal case of neurofibromatosis with hemothorax
نویسندگان
چکیده
منابع مشابه
Spontaneous Hemothorax in a Patient with Neurofibromatosis Type 1: A Case Report
Background: Neurofibromatosis type1 (NF-1) is a hereditary autosomal dominant disease that is accompanied by complications, such as benign and malignant tumors and vascular involvement, including pulmonary hypertension, artery stenosis, and pulmonary artery aneurysm. Spontaneous hemothorax is a rare and lethal complication of NF-1 due to vasculopathy as stenosis or aneurysmal modifications of l...
متن کاملA case of lethal spontaneous massive hemothorax in a patient with neurofibromatosis 1
Neurofibromatosis type 1 is an autosomal dominant disease characterized by multiple dermatological disorders amongst others. Among the less frequent manifestations are vascular abnormalities. Here, we present a case of spontaneous massive hemothorax in a 39-year-old Caucasian woman with neurofibromatosis 1 and a thoracic meningocele with a lethal outcome despite extensive surgical intervention ...
متن کاملA case report of neurofibromatosis
Introduction:Neurofibromatosis is a genetic disease characterized by multifocal benign tumors of peripheral nerves, called neurofibromas, and pigmented spots on the skin which inherited as autosomal-dominant. The most common form of the disease is neurofibromatosis type 1, also known as von Recklinghausen's disease of the skin. When an individual has small number of lesions in a limited region ...
متن کاملFatal hydrocephalus in a patient with neurofibromatosis.
To the Editor:-Anesthetic implications of neurofibromatosis may include airway, mediastid and vertebral neurofibromas, associated endocrine syndromes, and intracranial masses in 510% of patients. ’ Hydrocephalus is a rare manifestation of neurofibromatosis and is commonly descrihed during the first two decades of lie.’-* We present a case of acute postoperative hydrocephalus in a previously hea...
متن کاملBilateral Spontaneous Hemothorax with PNET: a case report and review
Background: Neuroectodermal Tumors (PNET) are malignant small cells neoplasm mainly occurring in children but can occur at any age. Extensive bleeding into the pleural cavity is rare In Children. Hemothorax would be compatible with a variety of congenital anomalies including sequestration, patent ductus artreiosus, and pulmonary arteriovenous malformation. Case report: A 2.5-years old girl who ...
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ژورنال
عنوان ژورنال: Trauma and Emergency Care
سال: 2019
ISSN: 2398-3345
DOI: 10.15761/tec.1000188